JUVENILE DERMATOMYOSITIS (JDM) | ABP Board Review скачать в хорошем качестве

JUVENILE DERMATOMYOSITIS (JDM) | ABP Board Review

This is a snippet from Dr. Andrea Sestak’s Rheumatology lecture in MedStudy’s 2023-2024 Pediatrics Video Board Review. https://medstudy.com/products/pediatr... JUVENILE DERMATOMYOSITIS (JDM) • Girls more commonly affected • Bimodal: 3–7 years of age and early teenage years • Rash with proximal muscle weakness – Classic heliotrope (faint purple to red discoloration of the eyelids) – Nailfold capillaritis – Seasonal clustering of onset ? infectious triggers Dermatomyositis • Gottron papules • Dystrophic calcification: calcinosis cutis • Proximal muscle weakness • Photosensitive rash DDx: SLE vs. JDM • Skin ulcerations are rare: can portend GI vasculitis - poor prognosis • Dysphagia, dysphonia can occur • No increased risk for malignancy in children • T2 or STIR image MRI of thighs can reveal myositis • Diagnosis – Heliotrope rash or Gottron papules + – 2 of the following for probable, 3 for definite diagnosis: • Symmetric proximal muscle weakness • ↑ CK, aldolase, LDH, transaminases • EMG abnormalities • Abnormal muscle biopsy • Rx: high-dose steroids 2–3 mg/kg/day (or pulse steroids IV methylprednisolone) • IVIG (monthly) • Hydroxychloroquine, MTX, CYA, MMF, IV CYP, combination DMARDs • Physical therapy • Sun avoidance • Refractory cases — rituximab, TNFi therapy Continue your review: https://medstudy.com/products/pediatr... Subscribe to our YouTube channel:    / @medstudycom   Follow us on: Instagram:   / medstudystrong   Facebook:   / medstudy   Twitter:   / medstudy   TikTok:   / medstudystrong   #Pediatricians #Pediatrician #Pediatrics #Peds #ABP #AOBP #boardexam #boardprep #meded #medicaleducation #rheumatology #rheumatologist