VSD-PA (Pulmonary Atresia With Ventricular Septal Defect)-İMAEH Zoom Dersleri-6 скачать в хорошем качестве

VSD-PA (Pulmonary Atresia With Ventricular Septal Defect)-İMAEH Zoom Dersleri-6

Pulmonary atresia with ventricular septal defect (PAVSD) is one of the cyanotic congenital heart diseases. It occurs due to under or maldevelopment of the right ventricular outflow tract along with atresia of the pulmonary valve and trunk. It also involves overriding of the aorta and a large ventricular septal defect. Previously it was termed as truncus arteriosus type IV. Whether it is a different entity or a severe form of Tetralogy of Fallot (TOF) is still controversial, but there is no denying the occurrence of PAVSD. The etiology of PAVSD is yet unknown. But several risk factors have been linked with the incidence of it. A genetic component has been suggested in literature but the level of evidence is weak.The incidence of congenital heart diseases is decreasing day by day because of the avoidance of known teratogens and risk factors by the patients through their education and counseling. The incidence of pulmonary atresia is also falling down. The prevalence of pulmonary atresia in the years 1999 to 2000 was 12.1% of all congenital heart diseases, which gradually went down to 9.6% in 2008 (p=0.01).