endolymphatic sac tumor ; Definition, Causes, Symptoms, Diagnosis, Treatment скачать в хорошем качестве

endolymphatic sac tumor ; Definition, Causes, Symptoms, Diagnosis, Treatment

An endolymphatic sac tumor (ELST) is a very rare and locally aggressive tumor that arises within the endolymphatic sac or duct, typically located in the inner ear. Here are some key points about ELSTs: Characteristics Type: Papillary epithelial neoplasm Location: Arises within the endolymphatic sac or duct, usually in the petrous bone of the temporal bone. Association: Strongly associated with von Hippel-Lindau (VHL) syndrome, a genetic disorder. Symptoms Hearing Loss: Progressive or fluctuating sensorineural hearing loss. Tinnitus: Ringing in the ears. Vertigo: Dizziness or loss of balance. Facial Paresis: Weakness or paralysis of facial muscles (less common). Other Symptoms: May include aural fullness and intralabyrinthine hemorrhage. Diagnosis Imaging: CT scans and MRI are used to detect and evaluate ELSTs. These imaging studies show bone erosion, hyperintensity, and heterogeneous enhancement1. Biopsy: A tissue sample may be taken to confirm the diagnosis. Treatment Surgical Excision: The primary treatment is surgical removal of the tumor. Early detection and intervention are crucial to prevent further hearing loss2. Radiation Therapy: May be used in conjunction with surgery for advanced cases. Prognosis Recurrence: ELSTs have a high recurrence rate if not completely excised. Survival Rate: The prognosis varies depending on the stage and location of the tumor, as well as the patient's overall health #endolymphaticsactumor