Abdominal manifestations of lymphangioleiomyomatosis (LAM) скачать в хорошем качестве

Abdominal manifestations of lymphangioleiomyomatosis (LAM)

Abdominal manifestations of LAM In more than 70% of LAM Renal angiomyolipoma (AML) Lymphangioleiomyoma Lymphadenopathy Ascites, thoracic duct dilatation, hepatic AML Uterine LAM, protein-losing enteropathy Often multiple, bilateral More frequent in LAM a/w tuberous sclerosis Fat poor AML: absence of fat does not preclude AML Usually asymptomatic Abdominal pain, hematuria, hemorrhage Lymphangioleiomyoma Smooth muscle proliferation  lymphatic obstruction Area of thicker wall than lymphangioma Cystic mass a/w LAM is likely a lymphangioleiomyoma Increasing size after diet or exercise, positional change Summary Renal or hepatic angiomyolipoma Lymphangioleiomyoma, lymphadenopathy Abdominal manifestations may be a first sign of LAM May be confused with other abdominal malignancy